Malformaciones arteriovenosas múltiples
DOI:
https://doi.org/10.59156/revista.v39i02.740Palabras clave:
Hemorragia intracraneal, Malformación arteriovenosa cerebral múltiple, Síndrome de Rendu-Osler-Weber, Síndrome de Wyburn-MasonResumen
Introducción: las malformaciones arteriovenosas (MAVs) suelen ser lesiones únicas; en ocasiones pueden presentarse de forma múltiple, asociadas a enfermedades congénitas.
Objetivos: realizar una actualización bibliográfica sobre las MAVs cerebrales múltiples y analizar su prevalencia, asociación a síndromes congénitos y la casuística de nuestra institución.
Conclusión: las MAVs cerebrales múltiples son poco frecuentes y requieren de un equipo multidisciplinario en su abordaje debido a su alta asociación a síndromes congénitos. Esta entidad representó el 1.27% del total de MAVs tratadas en nuestra institución y el 1.75% según lo reportado en diferentes series de casos publicadas previamente en la literatura. Se encontró con mayor frecuencia asociada a síndromes congénitos; el síndrome de Rendu-Osler-Weber fue el más común, presente en el 50% de los casos.
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